Protein basic information
LiverAtlas Protein ID |
HuLPr03636 |
Uniprot ID |
|
Uniprot Acc |
Q8N2K0;A6NED4;A6NJ90;A8K450;B4DE71;Q5T710;Q5T711;Q96CR1;Q9BX05;Q9NPX7;Q9UFV6; |
Protein name |
Monoacylglycerol lipase ABHD12 |
Comment |
FUNCTION:Has 2-arachidonoylglycerol hydrolase activity (By similarity). May be a regulator of endocannabinoid signaling pathways (By similarity).||CATALYTIC ACTIVITY:Hydrolyzes glycerol monoesters of long-chain fatty acids.||SUBCELLULAR LOCATION:Membrane; Single-pass membrane protein (By similarity).||ALTERNATIVE PRODUCTS:Event=Alternative splicing; Named isoforms=3; Name=1; IsoId=Q8N2K0-1; Sequence=Displayed; Name=2; IsoId=Q8N2K0-2; Sequence=VSP 009097; Name=3; IsoId=Q8N2K0-3; Sequence=VSP 037372;||PTM:Glycosylated (By similarity).||DISEASE:Defects in ABHD12 are the cause of polyneuropathy hearing loss ataxia retinitis pigmentosa and cataract (PHARC) [MIM:612674]. PHARC is a slowly progressive neurologic disorder with a variable phenotype resembling Refsum disease. Clinical features include sensorineural hearing loss, visual problems related to cataracts, retinitis pigmentosa, pes cavus, ataxic and/or spastic gait disturbances with a progressive sensorimotor peripheral neuropath |
Subcellular localization |
Membrane;Single-pass membrane protein(By similarity). |
Gene name |
|
Protein sequence
|
MRKRTEPVALEHERCAAAGSSSSGSAAAALDADCRLKQNL RLTGPAAAEPRCAADAGMKRALGRRKGVWLRLRKILFCV LGLYIAIPFLIKLCPGIQAKLIFLNFVRVPYFIDLKKPQ DQGLNHTCNYYLQPEEDVTIGVWHTVPAVWWKNAQGKDQ MWYEDALASSHPIILYLHGNAGTRGGDHRVELYKVLSSL GYHVVTFDYRGWGDSVGTPSERGMTYDALHVFDWIKARS GDNPVYIWGHSLGTGVATNLVRRLCERETPPDALILESP FTNIREEAKSHPFSVIYRYFPGFDWFFLDPITSSGIKFA NDENVKHISCPLLILHAEDDPVVPFQLGRKLYSIAAPAR SFRDFKVQFVPFHSDLGYRHKYIYKSPELPRILREFLGKSEPEHQH |
Database cross reference |
RefSeq Protein accession:NP_001035937
|
Liver relevance
HLPP validation |
Yes/No |
Yes |
Project name |
Chinese Liver;Human Liver Organelles; |
Ontology annotation
GO-C |
GO:0016021;C:integral to membrane;IEA:UniProtKB-KW. |
GO-F |
GO:0047372;F:acylglycerol lipase activity;IEA:EC. |
GO-P |
GO:0050896;P:response to stimulus;IEA:UniProtKB-KW. GO:0007601;P:visual perception;IEA:UniProtKB-KW. |