Protein basic information
LiverAtlas Protein ID |
HuLPr04032 |
Uniprot ID |
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Uniprot Acc |
P84996;A2A2S4; |
Protein name |
Protein ALEX |
Comment |
FUNCTION:May inhibit the adenylyl cyclase-stimulating activity of guanine nucleotide-binding protein G(s) subunit alpha which is produced from the same locus in a different open reading frame.||SUBUNIT:Interacts with the N-terminal region of the XLas isoforms of guanine nucleotide-binding protein G(s) subunit alpha (By similarity).||SUBCELLULAR LOCATION:Cell membrane; Peripheral membrane protein. Cell projection, ruffle (By similarity). Note=Predominantly associated with cell membrane ruffles (By similarity).||DISEASE:Defects in GNAS are the cause of GNAS hyperfunction (GNASHYP) [MIM:139320]. This condition is characterized by increased trauma-related bleeding tendency, prolonged bleeding time, brachydactyly and mental retardation. Both the XLas isoforms and the ALEX protein are mutated which strongly reduces the interaction between them and this may allow unimpeded activation of the XLas isoforms.||DISEASE:Defects in GNAS are a cause of ACTH-independent macronodular adrenal hyperplasi |
Subcellular localization |
Cell membrane;Peripheral membrane protein.Cell projection, ruffle(By similarity). |
Gene name |
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Protein sequence
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MMARPVDPQRSPDPTFRSSTRHSGKLEPMEATAHLLRKQC PSRLNSPAWEASGLHWSSLDSPVGSMQALRPSAQHSWSP EPSVVPDQAWEDTALHQKKLCPLSLTSLPREAAVNFSYR SQTLLQEAQVLQGSPELLPRSPKPSGLQRLAPEEATALP LRRLCHLSLMEKDLGTTAHPRGFPELSHKSTAAASSRQS RPRVRSASLPPRTRLPSGSQAPSAAHPKRLSDLLLTSRA AAPGWRSPDPRSRLAAPPLGSTTLPSTWTAPQSRLTARP SRSPEPQIRESEQRDPQLRRKQQRWKEPLMPRREEKYPL RGTDPLPPGQPQRIPLPGQPLQPQPILTPGQPQKIPTPG QHQPILTPGHSQPIPTPGQPLPPQPIPTPGRPLTPQPIP TPGRPLTPQPIQMPGRPLRLPPPLRLLRPGQPMSPQLRQ TQGLPLPQPLLPPGQPKSAGRPLQPLPPGPDARSISDPP APRSRLPIRLLRGLLARLPGGASPRAAAAAACTTMKGWP AATMTPAETSPTMGPPDASAGFSIGEIAAAESPSATYSA TFSCKPSGAASVDLRVPSPKPRALSRSRRYPWRRSADRC AKKPWRSGPRSAQRRNAVSSSTNNSRTKRWATCVRTACCF |
Database cross reference |
RefSeq Protein accession:NP_000507
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Liver relevance
HLPP validation |
Yes/No |
Yes |
Project name |
Human Liver Organelles; |
Ontology annotation
GO-C |
GO:0005886;C:plasma membrane;IEA:UniProtKB-SubCell. GO:0001726;C:ruffle;IEA:UniProtKB-SubCell. |
Pathway
Pathway name |