Protein basic information
LiverAtlas Protein ID |
HuLPr15425 |
Uniprot ID |
|
Uniprot Acc |
Q13231;Q0VGG5;Q0VGG6;Q3ZAR1;Q6ISC2;Q9H3V8;Q9UDJ8; |
Protein name |
Chitotriosidase-1 |
Comment |
FUNCTION:Degrades chitin, chitotriose and chitobiose. May participate in the defense against nematodes and other pathogens. Isoform 3 has no enzymatic activity.||CATALYTIC ACTIVITY:Random hydrolysis of N-acetyl-beta-D- glucosaminide (1->4)-beta-linkages in chitin and chitodextrins.||SUBUNIT:Monomer.||SUBCELLULAR LOCATION:Secreted. Lysosome. Note=A small proportion is lysosomal.||ALTERNATIVE PRODUCTS:Event=Alternative splicing; Named isoforms=3; Name=1; IsoId=Q13231-1; Sequence=Displayed; Name=2; IsoId=Q13231-2; Sequence=VSP 008631, VSP 008632; Name=3; IsoId=Q13231-3; Sequence=VSP 008633; Note=Duplication of 24 bp in exon 10 leads to the use of a cryptic splice site. The normal splice site is still present but not used;||TISSUE SPECIFICITY:Detected in spleen. Secreted by cultured macrophages.||POLYMORPHISM:A 24 bp duplication in exon 10 leads to the activation of an alternative splice site and the production of an inactive protein. About 6% of the population are deficient fo |
Subcellular localization |
Secreted.Lysosome. |
Gene name |
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Protein sequence
|
MVRSVAWAGFMVLLMIPWGSAAKLVCYFTNWAQYRQGEAR FLPKDLDPSLCTHLIYAFAGMTNHQLSTTEWNDETLYQE FNGLKKMNPKLKTLLAIGGWNFGTQKFTDMVATANNRQT FVNSAIRFLRKYSFDGLDLDWEYPGSQGSPAVDKERFTT LVQDLANAFQQEAQTSGKERLLLSAAVPAGQTYVDAGYE VDKIAQNLDFVNLMAYDFHGSWEKVTGHNSPLYKRQEES GAAASLNVDAAVQQWLQKGTPASKLILGMPTYGRSFTLA SSSDTRVGAPATGSGTPGPFTKEGGMLAYYEVCSWKGAT KQRIQDQKVPYIFRDNQWVGFDDVESFKTKVSYLKQKGL GGAMVWALDLDDFAGFSCNQGRYPLIQTLRQELSLPYLP SGTPELEVPKPGQPSEPEHGPSPGQDTFCQGKADGLYPN PRERSSFYSCAAGRLFQQSCPTGLVFSNSCKCCTWN |
Database cross reference |
RefSeq Protein accession:NP_003456
|
Liver relevance
HLPP validation |
Yes/No |
Yes |
Project name |
Human Liver Organelles; |
Ontology annotation
GO-C |
GO:0005615;C:extracellular space;IDA:UniProtKB. GO:0005764;C:lysosome;IEA:UniProtKB-SubCell. |
GO-F |
GO:0043169;F:cation binding;IEA:InterPro. GO:0008061;F:chitin binding;TAS:UniProtKB. GO:0008843;F:endochitinase activity;IDA:UniProtKB. |
GO-P |
GO:0006032;P:chitin catabolic process;IDA:UniProtKB. GO:0006955;P:immune response;NAS:UniProtKB. GO:0009617;P:response to bacterium;TAS:ProtInc. |
Pathway
Pathway name |