Protein basic information
LiverAtlas Protein ID |
HuLPr15811 |
Uniprot ID |
|
Uniprot Acc |
Q5EBM0;A2RUB0;A5D8T2;B7ZM18;Q6ZRU2;Q96AL8; |
Protein name |
UMP-CMP kinase 2, mitochondrial |
Comment |
FUNCTION:May participate in dUTP and dCTP synthesis in mitochondria. Is able to phosphorylate dUMP, dCMP, CMP, UMP and monophosphates of the pyrimidine nucleoside analogs ddC, dFdC, araC, BVDU and FdUrd with ATP as phosphate donor. Efficacy is highest for dUMP followed by dCMP; CMP and UMP are poor substrates. May be involved in mtDNA depletion caused by long term treatment with ddC or other pyrimidine analogs.||CATALYTIC ACTIVITY:ATP + (d)CMP = ADP + (d)CDP.||BIOPHYSICOCHEMICAL PROPERTIES:Kinetic parameters: KM=3.09 mM for CMP; KM=6.3 mM for UMP; KM=1.31 mM for dCMP; KM=0.1 mM for dUMP; Vmax=1.64 umol/min/mg enzyme towards CMP; Vmax=0.19 umol/min/mg enzyme towards UMP; Vmax=1.77 umol/min/mg enzyme towards dCMP; Vmax=0.48 umol/min/mg enzyme towards dUMP;||SUBCELLULAR LOCATION:Mitochondrion.||ALTERNATIVE PRODUCTS:Event=Alternative splicing; Named isoforms=4; Name=1; IsoId=Q5EBM0-1; Sequence=Displayed; Name=2; IsoId=Q5EBM0-2; Sequence=VSP 033238, VSP 033239; Note=No |
Subcellular localization |
Mitochondrion. |
Gene name |
|
Protein sequence
|
MAFARRLLRGPLSGPLLGRRGVCAGAMAPPRRFVLELPDC TLAHFALGADAPGDADAPDPRLAALLGPPERSYSLCVPV TPDAGCGARVRAARLHQRLLHQLRRGPFQRCQLLRLLCY CPGGQAGGAQQGFLLRDPLDDPDTRQALLELLGACQEAP RPHLGEFEADPRGQLWQRLWEVQDGRRLQVGCAQVVPVP EPPLHPVVPDLPSSVVFPDREAARAVLEECTSFIPEARA VLDLVDQCPKQIQKGKFQVVAIEGLDATGKTTVTQSVAD SLKAVLLKSPPSCIGQWRKIFDDEPTIIRRAFYSLGNYI VASEIAKESAKSPVIVDRYWHSTATYAIATEVSGGLQHL PPAHHPVYQWPEDLLKPDLILLLTVSPEERLQRLQGRGM EKTREEAELEANSVFRQKVEMSYQRMENPGCHVVDASPS REKVLQTVLSLIQNSFSEP |
Database cross reference |
RefSeq Protein accession:NP_997198
|
Liver relevance
HLPP validation |
Yes/No |
Yes |
Project name |
Human Liver Organelles; |
Ontology annotation
GO-C |
GO:0005739;C:mitochondrion;IDA:MGI. |
GO-F |
GO:0005524;F:ATP binding;IEA:UniProtKB-KW. GO:0004127;F:cytidylate kinase activity;IDA:MGI. GO:0004798;F:thymidylate kinase activity;IEA:InterPro. GO:0033862;F:UMP kinase activity;IDA:MGI. |
GO-P |
GO:0006233;P:dTDP biosynthetic process;IEA:InterPro. |
Pathway
Pathway name |