Protein basic information
LiverAtlas Protein ID |
HuLPr16154 |
Uniprot ID |
|
Uniprot Acc |
Q6ZWL3;B7U6W2;Q6ZTM4; |
Protein name |
Cytochrome P450 4V2 |
Comment |
FUNCTION:Unknown. May have a role in fatty acid and steroid metabolism.||COFACTOR:Heme group (By similarity).||SUBCELLULAR LOCATION:Endoplasmic reticulum membrane; Single-pass membrane protein (Potential).||ALTERNATIVE PRODUCTS:Event=Alternative splicing; Named isoforms=2; Name=1; IsoId=Q6ZWL3-1; Sequence=Displayed; Name=2; IsoId=Q6ZWL3-2; Sequence=VSP 014918; Note=No experimental confirmation available;||TISSUE SPECIFICITY:Broadly expressed. Detected in heart, brain, placenta, lung, liver, skeletal muscle, kidney, pancreas, retina, retinal pigment epithelium (RPE) and lymphocytes.||DISEASE:Defects in CYP4V2 are a cause of Bietti crystalline corneoretinal dystrophy (BCD) [MIM:210370]. BCD is an autosomal recessive retinal dystrophy characterized by multiple glistening intraretinal crystals scattered over the fundus, a characteristic degeneration of the retina, and sclerosis of the choroidal vessels, ultimately resulting in progressive night blindness and constriction of the visua |
Subcellular localization |
Endoplasmic reticulum membrane;Single-pass membrane protein(Potential). |
Gene name |
|
Protein sequence
|
MAGLWLGLVWQKLLLWGAASALSLAGASLVLSLLQRVASY ARKWQQMRPIPTVARAYPLVGHALLMKPDGREFFQQIIE YTEEYRHMPLLKLWVGPVPMVALYNAENVEVILTSSKQI DKSSMYKFLEPWLGLGLLTSTGNKWRSRRKMLTPTFHFT ILEDFLDIMNEQANILVKKLEKHINQEAFNCFFYITLCA LDIICETAMGKNIGAQSNDDSEYVRAVYRMSEMIFRRIK MPWLWLDLWYLMFKEGWEHKKSLQILHTFTNSVIAERAN EMNANEDCRGDGRGSAPSKNKRRAFLDLLLSVTDDEGNR LSHEDIREEVDTFMFEGHDTTAAAINWSLYLLGSNPEVQ KKVDHELDDVFGKSDRPATVEDLKKLRYLECVIKETLRL FPSVPLFARSVSEDCEVAGYRVLKGTEAVIIPYALHRDP RYFPNPEEFQPERFFPENAQGRHPYAYVPFSAGPRNCIG QKFAVMEEKTILSCILRHFWIESNQKREELGLEGQLILR PSNGIWIKLKRRNADER |
Database cross reference |
RefSeq Protein accession:NP_997235
|
Liver relevance
HLPP validation |
Yes/No |
Yes |
Project name |
Chinese Liver;Human Liver Organelles; |
Ontology annotation
GO-C |
GO:0005789;C:endoplasmic reticulum membrane;IEA:UniProtKB-SubCell. GO:0016021;C:integral to membrane;IEA:UniProtKB-KW. |
GO-F |
GO:0009055;F:electron carrier activity;IEA:InterPro. GO:0020037;F:heme binding;IEA:InterPro. GO:0004497;F:monooxygenase activity;IEA:UniProtKB-KW. |
GO-P |
GO:0055114;P:oxidation-reduction process;IEA:UniProtKB-KW. GO:0050896;P:response to stimulus;IEA:UniProtKB-KW. GO:0007601;P:visual perception;IEA:UniProtKB-KW. |