Protein basic information
LiverAtlas Protein ID |
HuLPr21657 |
Uniprot ID |
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Uniprot Acc |
Q9H6L5;Q69YN8;Q9H6K6;Q9H764;Q9NXM8; |
Protein name |
Protein FAM134B |
Comment |
FUNCTION:Required for long-term survival of nociceptive and autonomic ganglion neurons.||SUBCELLULAR LOCATION:Golgi apparatus, cis-Golgi network membrane; Multi-pass membrane protein (By similarity).||ALTERNATIVE PRODUCTS:Event=Alternative splicing; Named isoforms=2; Name=1; IsoId=Q9H6L5-1; Sequence=Displayed; Name=2; IsoId=Q9H6L5-2; Sequence=VSP 025685, VSP 025686;||DISEASE:Defects in FAM134B are the cause of hereditary sensory and autonomic neuropathy type 2B (HSAN2B) [MIM:613115]. A form of hereditary sensory and autonomic neuropathy, a genetically and clinically heterogeneous group of disorders characterized by degeneration of dorsal root and autonomic ganglion cells, and by sensory and/or autonomic abnormalities. HSAN2B is an autosomal recessive disorder characterized by impairment of pain, temperature and touch sensation. Onset occurs in the first or second decade, with impaired nociception and progressive mutilating ulceration of the hands and feet with osteomyelitis and acr |
Subcellular localization |
Golgi apparatus, cis-Golgi network membrane;Multi-pass membrane protein(By similarity). |
Gene name |
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Protein sequence
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MASPAPPEHAEEGCPAPAAEEQAPPSPPPPQASPAERQQQ EEEAQEAGAAEGAGLQVEEAAGRAAAAVTWLLGEPVLWL GCRADELLSWKRPLRSLLGFVAANLLFWFLALTPWRVYH LISVMILGRVIMQIIKDMVLSRTRGAQLWRSLSESWEVI NSKPDERPRLSHCIAESWMNFSIFLQEMSLFKQQSPGKF CLLVCSVCTFFTILGSYIPGVILSYLLLLCAFLCPLFKC NDIGQKIYSKIKSVLLKLDFGIGEYINQKKRERSEADKE KSHKDDSELDFSALCPKISLTVAAKELSVSDTDVSEVSW TDNGTFNLSEGYTPQTDTSDDLDRPSEEVFSRDLSDFPS LENGMGTNDEDELSLGLPTELKRKKEQLDSGHRPSKETQ SAAGLTLPLNSDQTFHLMSNLAGDVITAAVTAAIKDQLE GVQQALSQAAPIPEEDTDTEEGDDFELLDQSELDQIESE LGLTQDQEAEAQQNKKSSGFLSNLLGGH |
Database cross reference |
RefSeq Protein accession:NP_001030022
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Liver relevance
HLPP validation |
Yes/No |
Yes |
Project name |
Human Liver Organelles; |
Ontology annotation
GO-C |
GO:0005801;C:cis-Golgi network;ISS:UniProtKB. GO:0005783;C:endoplasmic reticulum;IEA:InterPro. GO:0016021;C:integral to membrane;IEA:UniProtKB-KW. |
GO-P |
GO:0019233;P:sensory perception of pain;IMP:UniProtKB. |