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Protein basic information

LiverAtlas Protein ID

HuLPr34037

Uniprot ID

Q53ZP6_HUMAN

Uniprot Acc

Q53ZP6;

Protein name

Uroporphyrinogen decarboxylase

Comment

CATALYTIC ACTIVITY:Uroporphyrinogen III = coproporphyrinogen + 4 CO(2).||PATHWAY:Porphyrin metabolism; protoporphyrin-IX biosynthesis; coproporphyrinogen III from 5-aminolevulinate:step 4/4.||SIMILARITY:Belongs to the uroporphyrinogen decarboxylase family.

Gene name

uroporphyrinogen decarboxylase

Protein sequence

MEANGLGPQGFPELKNDTFLRAAWGEETDYTPVWCMRQAG RYLPEFRETRAAQDFFSTCRSPEACCELTLQPLRRFLLD AAIIFSDILVVPQALGMEVTMVPGKGPSFPEPLREEQDL ERLRDPEVVASELGYVFQAITLTRQRLAGRVPLIGFAGA PWTLMTYMVEGGGSSTMAQAKRWLYQRPQASHQLLRILT DALVPYLVGQVVAGAQALQLFESHAGHLGPQLFNKFALP YIRDVAKQVKARLREAGLAPVPMIIFAKDGHFALEELAQ AGYEVVGLDWTVAPKKARECVGKTVTLQGNLDPCALYAS EEEIGQLVKQMLDDFGPHRYIANLGHGLYPDMDPEHVGA FVDAVHKHSRLLRQN

Database cross reference

RefSeq Protein accession:NP_000365
RefSeq Protein gi:71051616

Liver relevance

HLPP validation

Yes/No

Yes

Project name

Chinese Liver;French Liver;Human Fetal Liver;Human Liver Organelles;

Ontology annotation

GO-C

GO:0005737;C:cytoplasm;IDA:HPA. GO:0015630;C:microtubule cytoskeleton;IDA:HPA. GO:0005634;C:nucleus;IDA:HPA.

GO-F

GO:0004853;F:uroporphyrinogen decarboxylase activity;IEA:HAMAP.

GO-P

GO:0006779;P:porphyrin biosynthetic process;IEA:HAMAP.